This is the case of a 46-year-old man with Steinert’s disease brought to our center with syncope preceded by thoracic pain. The baseline EKC revealed the presence of sinus tachycardia, first degree AV block, and left bundle branch block (Fig. 1A). During the cardiac examination, the patient developed an episode of syncope. Also, ventricular fibrillation was confirmed (Fig. 1B) that was solved after the administration of a 200J discharge. An emergency coronary angiography revealed the presence of normal coronary arteries (Fig. 2, videos 1 and 2) being ventriculography compatible with inverted Tako-Tsubo cardiomyopathy (Fig. 3, video 3). The enzymatic mobilization of cardiac biomarkers (hs-tnI) was discrete. One month after hospital discharge, the patient was assessed at the doctor’s office and the transthoracic echocardiogram performed looked normal.

Figure 1

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Figure 2

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Figure 3

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